These statistics on pulmonary fibrosis in the UK were compiled as part of our Respiratory Health of the Nation project by teams at St George’s, University of London, Nottingham University and Imperial College London.
Note on IPF prevalence and incidence data
IPF prevalence and incidence data need to be treated with caution. This is due to:
- The range of possible codings that could be used by health care professionals to record IPF.
- The changes that have been made to the way IPF is coded. These take time to become standard practice and therefore impact on the data recorded.
To decide which codings to use, we consulted leading epidemiologists and IPF clinicians. Other interpretations of the base data may yield different results.
The primary care codes that we used to identify IPF were:
- H563.00 : Idiopathic fibrosing alveolitis
- H563.11 : Hamman-Rich syndrome
- H563.12 : Cryptogenic fibrosing alveolitis
- H563.13 : Idiopathic pulmonary fibrosis
- H563100 : Diffuse pulmonary fibrosis
- H563300 : Usual interstitial pneumonitis
- H563z00 : Idiopathic fibrosing alveolitis not otherwise specified
- H563200 : Pulmonary fibrosis
Incidence figures for 2012 have been omitted from some of the analyses. This is because changes in the diagnostic coding used to record the disease led to a significant rise in recorded incidence.
It is unlikely that this reflects a real change in incidence. With the above caveats, our clinical and epidemiological experts believe the figures presented here provide an accurate picture of IPF in the UK.